Periodic fever syndromes: a patient diagnosed with recurrent Kawasaki disease
Makaleler > Tam Makale · 2020
Yazarlar: Sena Turk, Derya Aydin, Eser Dogan, Reşit Ertürk LEVENT, Necil KÜTÜKÇÜLER
Cardiology in the Young, Uluslararası, Wos, 2020, cilt 30, ss 1009-1011
DOI: 10.1017/s1047951120001444
Özet
Kawasaki disease, known as mucocutaneous lymph node syndrome, is a multi-system disease of unknown aetiology that occurs in young children under 5 years of age. The recurrence rate of Kawasaki disease is as rare as 1-3%. Especially in cases with coronary artery involvement, recurrent Kawasaki disease should be investigated in terms of underlying rheumatologic diseases such as periodic fever syndromes, microscopic polyangiitis, polyarteritis nodosa, and systemic-onset juvenile arthritis. In this study, we report homozygote mutations in mevalonate kinase and familial Mediterranean fever genes in a recurrent Kawasaki disease with coronary dilatation.