Right ventricular endomyocardial fibrosis mimicking Ebstein anomaly in a patient with Behcet's disease: case report and review of the literature
Articles > Review · 2014
Authors: Ali Buturak, Özlem SAYGILI, Sila Ulus, Melike Kalfa, Hasan Karabulut, Cem ALHAN, Sinan DAĞDELEN, Kenan AKSU
MODERN RHEUMATOLOGY, Journal Indexed in SCI Expanded, International, 2014, vol 24, pp 532-536
DOI: 10.3109/14397595.2013.874731
Summary
Behcet's disease is a multisystemic, chronic inflammatory disorder with diffuse clinical manifestations including the cardiovascular system. Endomyocardial fibrosis is a rarely seen complication of Behcet's disease leading to progressive heart failure. We report a case of right ventricular endomyocardial fibrosis mimicking Ebstein anomaly in a 26-year-old male Turkish patient with Behcet's disease, who had heart failure symptoms. In addition, the previously reported cases of endomyocardial fibrosis complicating Behcet's disease are reviewed in this article.