Natural History of Congenital Generalized Lipodystrophy: A Nationwide Study From Turkey

Articles > Article · 2016

Authors: Bans Akinci, HÜSEYİN ONAY, Tevfik Demir, Samim ÖZEN, Hulya Kayserili, Gulcin AKİNCİ, Banu Nur, Beyhan Tuysuz, Mehmet Nun Ozbek, Adem Gungor, Ilgın YILDIRIM ŞİMŞİR, Canan Altay, Leyla Demir, Enver Simsek, Murat Atmaca, Haluk Topaloglu, Habib BİLEN, Hulusi Atmaca, Tahir ATİK, Umit Cavdar, Umut Altunoglu, Ayca Aslanger, Ercan Mihci, Mustafa Secil, Lütfiye Füsun SAYGILI, Abdurrahman Comlekci, Abhimanyu Garg

JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM, Journal Indexed in SCI Expanded, International, 2016, vol 101, pp 2759-2767

DOI: 10.1210/jc.2016-1005

Summary

Context: Congenital generalized lipodystrophy (CGL) is a rare autosomal recessive disorder characterized by near-total lack of body fat.

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