Weaning practices in phenylketonuria vary between health professionals in Europe
Articles > Article · 2019
Authors: A. Pinto, S. Adams, K. Ahring, H. Allen, M. F. Almeida, D. Garcia-Arenas, N. Arslan, M. Assoun, Yasemin Hande ATİK ALTINOK, D. Barrio-Carreras, A. Belanger Quintana, S. M. Bernabei, C. Bontemps, F. Boyle, G. Bruni, M. Bueno-Delgado, G. Caine, R. Carvalho, A. Chrobot, K. Chyz, B. Cochrane, C. Correia, K. Corthouts, A. Daly, S. De Leo, A. Desloovere, A. De Meyer, A. De Theux, B. Didycz, M. E. Dijsselhof, K. Dokoupil, J. Drabik, C. Dunlop, W. Eberle-Pelloth, K. Eftring, J. Ekengrena, I. Errekalde, S. Evans, A. Foucart, L. Fokkema, L. Francois, M. French, E. Forssell, C. Gingell, C. Goncalves, H. Gokmen Ozel, A. Grimsley, G. Gugelmo, E. Gyure, C. Heller, R. Hensler, I. Jardim, C. Joost, M. Joerg-Streller, C. Jouault, A. Jung, M. Kanthe, N. Koc, I. L. Kok, T. Kozanoglu, B. Kumru, F. Lang, K. Lang, I. Liegeois, A. Liguori, R. Lilje, O. Lubina, P. Manta-Vogli, D. Mayr, C. Meneses, C. Newby, U. Meyer, S. Mexia, C. Nicol, U. Och, S. M. Olivas, C. Pedron-Giner, R. Pereira, K. Plutowska-Hoffmann, J. Purves, A. Re Dionigi, K. Reinson, M. Robert, L. Robertson, J. C. Rocha, C. Rohde, S. Rosenbaum-Fabian, A. Rossi, M. Ruiz, J. Saligova, A. Gutierrez-Sanchez, A. Schlune, K. Schulpis, J. Serrano-Nieto, A. Skarpalezou, R. Skeath, A. Slabbert, K. Straczek, M. Gizewska, A. Terry, J. Tuokkola
MOLECULAR GENETICS AND METABOLISM REPORTS, Journal Indexed in SCI Expanded, International, 2019, vol 18, pp 39-44
DOI: 10.1016/j.ymgmr.2018.11.003
Summary
Background: In phenylketonuria (PKU), weaning is considered more challenging when compared to feeding healthy infants. The primary aim of weaning is to gradually replace natural protein from breast milk or standard infant formula with solids containing equivalent phenylalanine (Phe). In addition, a Phe-free second stage L-amino acid supplement is usually recommended from around 6 months to replace Phe-free infant formula. Our aim was to assess different weaning approaches used by health professionals across Europe.