Peroral Endoscopic Myotomy in Pediatric Triple A Syndrome: Report of Three Cases
Articles > Article · 2025
Authors: Ali Cagatay Bozkina, Abdullah Murat BUYRUK
Revista Española de Enfermedades Digestivas, International, WoS, 2025, vol 117, pp 803-804
DOI: 10.17235/reed.2025.11589/2025
Summary
Triple A syndrome (Allgrove syndrome) is a rare inherited disorder characterized by adrenal insufficiency, alacrima, and achalasia. Despite POEM's established role in achalasia management, its effectiveness in Triple A syndrome remains largely undefined, as fewer than 10 cases have been reported. We present three genetically confirmed pediatric Triple A patients (two males, one female; 11-16 years) with long-standing achalasia, all with Eckardt scores of 12 on admission and successfully treated with POEM after failing conventional therapies.