Peroral Endoscopic Myotomy in Pediatric Triple A Syndrome: Report of Three Cases
Makaleler > Tam Makale · 2025
Yazarlar: Ali Cagatay Bozkina, Abdullah Murat BUYRUK
Revista Española de Enfermedades Digestivas, Uluslararası, Wos, 2025, cilt 117, ss 803-804
DOI: 10.17235/reed.2025.11589/2025
Özet
Triple A syndrome (Allgrove syndrome) is a rare inherited disorder characterized by adrenal insufficiency, alacrima, and achalasia. Despite POEM's established role in achalasia management, its effectiveness in Triple A syndrome remains largely undefined, as fewer than 10 cases have been reported. We present three genetically confirmed pediatric Triple A patients (two males, one female; 11-16 years) with long-standing achalasia, all with Eckardt scores of 12 on admission and successfully treated with POEM after failing conventional therapies.