Primary Ovarian Rhabdomyosarcoma Coexisting with Pseudo-Meigs’ Syndrome in a Young Patient: A Case Report and Brief Literature Review
Makaleler > Tam Makale · 2019
Yazarlar: Şule GÖKÇE, Nuri Zafer KURUGÖL, Elvin Orujov, Gürdeniz SERİN
Türk Pediatri Arşivi, SCI Expanded İndekslerine Giren Dergi, Uluslararası, Scopus, 2019, cilt 55, ss 203-206
DOI: 10.14744/turkpediatriars.2019.82474
Özet
Primary rhabdomyosarcoma is one of the malignant soft tissue sarcomas of childhood originating from embryonic mesenchyme. The tumor can occur in the head, neck region, and limbs, and genitourinary system. Primary ovarian rhabdomyosarcoma is an extremely rare malignancy with a few documented pediatric patients in the literature. Pseudo-Meigs' syndrome is a type of Meigs' syndrome that is usually associated with other benign ovarian tumors or any other type of malignant tumors. It is a rare condition characterized by ascites, pleural effusion, benign ovarian tumors or fibroma-like tumors, and resolution of ascites and pleural effusion after the removal of the tumor. A patient of Asian origin came to our clinic with symptoms of mild dyspnea, and gradually increasing abdominal swelling. Magnetic resonance imaging scans indicated masses with solid cystic components on both ovaries with a suspicion of malignancy, showing bilateral pleural effusion and massive ascites. This is the first reported case of a pure primary ovarian rhabdomyosarcoma associated with a Pseudo-Meigs syndrome in a young girl.