Recurrent systemic thromboembolism in paediatric restrictive cardiomyopathy: a case highlighting the need for early anticoagulation and transplant evaluation

Makaleler > Tam Makale · 2026

Yazarlar: Hakan Kurt, Zulal Ulger, Tülay Öztürk, Reşit Ertürk LEVENT, Eser Doğan

Cardiology in the Young, Uluslararası, Wos, 2026, cilt 36, ss 653-656

DOI: 10.1017/s1047951126111871

Özet

Restrictive cardiomyopathy is a rare paediatric myocardial disorder causing diastolic dysfunction with preserved systolic function. We report a 14-year-old girl with idiopathic restrictive cardiomyopathy and recurrent systemic thromboemboli (stroke, limb ischaemia, renal infarction, and intracardiac thrombi) despite sinus rhythm. Anticoagulation resolved thrombi. She is currently awaiting heart transplantation. Early recognition, prompt anticoagulation, genetic evaluation, and consideration for transplantation are essential to optimise outcomes.

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