Early feeding practices in infants with phenylketonuria across Europe
Articles > Article · 2018
Authors: A. Pinto, S. Adams, K. Ahring, H. Allen, M. F. Almeida, D. Garcia-Arenas, N. Arslan, M. Assoun, Yasemin Hande ATİK ALTINOK, D. Barrio-Carreras, A. Belanger Quintana, S. M. Bernabei, C. Bontemps, F. Boyle, G. Bruni, M. Bueno-Delgado, G. Caine, R. Carvalho, A. Chrobot, K. Chyz, B. Cochrane, C. Correia, K. Corthouts, A. Daly, S. De Leo, A. Desloovere, A. De Meyer, A. De Theux, B. Didycz, M. E. Dijsselhof, K. Dokoupil, J. Drabik, C. Dunlop, W. Eberle-Pelloth, K. Eftring, J. Ekengren, I. Errekalde, S. Evans, A. Foucart, L. Fokkema, L. Francois, M. French, E. Forssell, C. Gingell, C. Goncalves, H. Gokmen Ozel, A. Grimsley, G. Gugelmo, E. Gyure, C. Heller, R. Hensler, I. Jardim, C. Joost, M. Joerg-Streller, C. Jouault, A. Jung, M. Kanthe, N. Koc, I. L. Kok, T. Kozanoglu, B. Kumru, F. Lang, K. Lang, I. Liegeois, A. Liguori, R. Lilje, O. Lubina, P. Manta-Vogli, D. Mayr, C. Meneses, C. Newby, U. Meyer, S. Mexia, C. Nicol, U. Och, S. M. Olivas, C. Pedron-Giner, R. Pereira, K. Plutowska-Hoffmann, J. Purves, A. Re Dionigi, K. Reinson, M. Robert, L. Robertson, J. C. Rocha, C. Rohde, S. Rosenbaum-Fabian, A. Rossi, M. Ruiz, J. Saligova, A. Gutierrez-Sanchez, A. Schlune, K. Schulpis, J. Serrano-Nieto, A. Skarpalezou, R. Skeath, A. Slabbert, K. Straczek, M. Gizewska, A. Terry, J. Tuokkola
MOLECULAR GENETICS AND METABOLISM REPORTS, Journal Indexed in SCI Expanded, International, 2018, vol 16, pp 82-89
DOI: 10.1016/j.ymgmr.2018.07.008
Summary
Background: In infants with phenylketonuria (PKU), dietary management is based on lowering and titrating phenylalanine (Phe) intake from breast milk or standard infant formula in combination with a Phe-free infant formula in order to maintain blood Phe levels within target range. Professionals use different methods to feed infants with PKU and our survey aimed to document practices across Europe.