Therapy resistant idiopathic scleredema: an underlying pathology not always present
Articles > Case Report · 2015
Authors: Melike Kalfa, Hayriye Kocanaoğulları, Figen YARGUCU ZİHNİ, Gonca KARABULUT, Hakan Emmungil, Vedat İnal
EUROPEAN JOURNAL OF RHEUMATOLOGY, Journal Indexed in ESCI, International, Emerging Sources Citation Index (ESCI), 2015, vol 2, pp 163-164
Summary
<p>Scleredema is a rare connective tissue disorder of unknown pathogenesis. Three types of scleredema have been described, based on its association with postinfection, monoclonal gammopathy and diabetes mellitus. We report herein a case of scleredema which the diagnosis didn't get specified. The patient was followed regularly for 13 years and did not respond to various combinations of immuno-suppressants and psoralen plus ultraviolet A therapy. Treatment of scleredema is quite difficult and of limited success. At present, there is no proved treatment for this disease.</p>