Jaffe Lichtenstein Type of Polyostotic Skeletal Fibrous Dysplasia With the Involvement of Cranial Bones
Articles > Article · 2021
Authors: Ozlem Akkemik, Serkan Erkus, Onder Kalenderer, Nesrin DÜNDAR
JOURNAL OF CRANIOFACIAL SURGERY, Journal Indexed in SCI Expanded, International, 2021, vol 32, pp e705-e708
DOI: 10.1097/scs.0000000000007700
Summary
Fibrous dysplasia (FD), a benign fibro-osseous bone tumor commonly involving the craniofacial region, presents a wide spectrum of radiographic patterns. When FD lesions are suspected, various imaging modalities and histopathologic analyses may be required to reach a firm diagnosis. Here, the authors report the case of a 10-year-old male patient presenting with polyostotic type of FD with follow-up data for the next 9 years. The patient showed involvement of cranial bones and bilateral femurs, with skin pigmentation and no endocrine disease, consistent with the diagnosis of Jaffe Lichtenstein disease. The craniofacial radiographic features obtained with computed tomography and cone-beam computerized tomography are documented in this article.