Therapy resistant idiopathic scleredema: an underlying pathology not always present
Makaleler > Tam Makale · 2015
Yazarlar: Melike KALFA, Hayriye KOÇANAOĞULLARI, Figen YARGUCU ZİHNİ, Gonca KARABULUT, Hakan EMMUNGİL, VEDAT İNAL
EUROPEAN JOURNAL OF RHEUMATOLOGY, SCI Expanded İndekslerine Giren Dergi, Uluslararası, 2015, cilt 2, ss 163-164
DOI: 10.5152/eurjrheum.2015.0004
Özet
Scleredema is a rare connective tissue disorder of unknown pathogenesis. Three types of scleredema have been described, based on its association with postinfection, monoclonal gammopathy and diabetes mellitus. We report herein a case of scleredema which the diagnosis didn't get specified. The patient was followed regularly for 13 years and did not respond to various combinations of immuno-suppressants and psoralen plus ultraviolet A therapy. Treatment of scleredema is quite difficult and of limited success. At present, there is no proved treatment for this disease.