Worldwide survey of T2* cardiovascular magnetic resonance in Thalassaemia

Makaleler > Tam Makale · 2011

Yazarlar: John-Paul Carpenter, Taigang He, Paul Kirk, Lisa Anderson, John B Porter, Malcolm Walker, Renzo Galanello, Fabrice Danjou, Gianluca Forni, Antonis Kattamis, Vassilis Ladis, Marouso Drossou, Demetra Vini, Andreas Michos, Vassilios Perifanis, Tuncay Hazirolan, Ana Almeida, Yeşim AYDINOK, Mirella Rangelova, Amal El-Beshlawy, Mohsen Elalfy, Ibrahim Alnasser, Shahina Daar, Juliano de Lara Fernandes, Dudley J Pennell

Journal of Cardiovascular Magnetic Resonance, Uluslararası, Wos, 2011, cilt 13

DOI: 10.1186/1532-429x-13-s1-o15

Özet

Thalassaemia major (TM) affects hundreds of thousands of patients worldwide but only a minority have access to regular blood transfusion and chelation therapy. Cardiovascular magnetic resonance (CMR) T2* measurement provides an accurate, reproducible measurement of cardiac iron which is the cause of heart failure and early death in many transfused TM patients. This technique has been adopted as part of routine management in many countries where survival is now approaching normal but little is known about the severity and effects of myocardial iron loading in different geographical regions.

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