Right ventricular endomyocardial fibrosis mimicking Ebstein anomaly in a patient with Behçet’s disease: case report and review of the literature
Articles > Article · 2012
Authors: Ali Buturak, Ozlem Saygili, Sıla Ulus, Melike Kalfa, Hasan Karabulut, Cem Alhan, Sinan Dagdelen, Kenan AKSU
Modern Rheumatology, International, WoS, 2012
DOI: 10.1007/s10165-012-0801-z
Summary
Behçet’s disease is a multisystemic, chronic inflammatory disorder with diffuse clinical manifestations including the cardiovascular system. Endomyocardial fibrosis is a rarely seen complication of Behçet’s disease leading to progressive heart failure. We report a case of right ventricular endomyocardial fibrosis mimicking Ebstein anomaly in a 26-year-old male Turkish patient with Behçet’s disease, who had heart failure symptoms. In addition, the previously reported cases of endomyocardial fibrosis complicating Behçet’s disease are reviewed in this article.